Introduction: The relationship between dyslipidemia and hearing is controversial, especially in children as data are scarce and limited to case reports. We sought to determine whether dyslipidemia is associated with sensorineural hearing loss (SNHL) in a group of 5-18 year old children and adolescents. Materials and Methods. Records of all 5 to 18 year old children who attended the pediatric endocrinology clinic of Loghman Hospital in Tehran, Iran, between April 2007 and April 2009, were reviewed. Records with a lipid profile were obtaimed and following confirmation of their lipid profiles, they were enrolled if the results were the same as before (normal or dyslipidemic). Pure tone thresholds, speech discrimination score and lipid profiles were analyzed. Results. When controlled for age and sex, no associations between dyslipidemia and SNHL were found. There was also no statistically significant relationship between dyslipidemia and SNHL in different age groups. Conclusion. No association was found between dyslipidemia and SNHL in children and adolescents aged 5 to 18 years.